Amyotrophic Lateral Sclerosis (ALS)
Patients will be considered to be in the terminal stage
of ALS if they meet the following criteria: should fulfill 1
2 or 3 should be present; factors
from 3
-
Patient should demonstrate critically impaired
breathing capacity as demonstrated by all the
following characteristics occurring within the 12
months preceding initial hospice certification:
- • FVC < 40% of normal.
- • Dyspnea at rest.
- • Patient declines mechanical ventilation; external
ventilation used for comfort measures only.
- • No invasive ventilation.
-
If unable to perform the FVC test, patient
should demonstrate BOTH:
- A)
Rapid progression of ALS as demonstrated by all
the following characteristics occurring within the
12 months preceding initial hospice certification:
- • Progression from independent ambulation
to wheelchair to bed-bound status.
- • Progression from normal to barely intelligible
or unintelligible speech.
- • Progression from normal to pureed diet.
- • Progression from independence in most or all activities
of daily living (ADLs) to needing major assistance by
caretaker in all ADLs.
- • Difficulty breathing at rest or a respiratory rate
greater
than 20 breaths per minute.
- • Unexplained confusion or anxiety.
- • Weakening cough.
- B)
Critical nutritional impairment as demonstrated by all the
following characteristics occurring within the 12 months
preceding initial hospice certification:
- • Oral intake of nutrients and fluids insufficient to
sustain life.
- • Difficulty swallowing with a continuing weight
loss of 5% or more.
- • Dehydration or hypovolemia.
- • Absence of artificial feeding methods, sufficient to
sustain life, but not for relieving hunger.
-
Patient should demonstrate BOTH:
- A)
Rapid progression of ALS, see 2.a above
- B)
Life-threatening complications as demonstrated by one
of the following characteristics occurring within the 12
months preceding initial hospice certification:
- • Recurrent aspiration pneumonia (with or without
tube feedings); upper urinary tract infection, e.g.,
pyelonephritis, sepsis; recurrent fever or infection
after antibiotic therapy; Stage 3 or 4 decubitus ulcer(s).